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Susac Syndrome

Rare autoimmune microangiopathy involving brain, retina, and inner ear together.

Written by: Saygı Hospital Health Guide Editorial Board
Last updated:

This content has been compiled by the Saygı Hospital Health Guide Editorial Board and is periodically reviewed by a specialist physician.

References (5)

This content is for informational purposes only and does not constitute medical advice. You can book an appointment at our Nöroloji department. Book Appointment →

What is Susac Syndrome?

Susac syndrome is a rare disease in which the brain, retina, and inner ear are commonly affected as a result of autoimmune endotheliopathy of small vessels.

It is usually seen in young women and is recognized by the triad of encephalopathy, branch retinal artery occlusions, and sensorineural hearing loss.

The typical 'snowball' appearance in the inner part of the corpus callosum on MRI assists in diagnosis.

Symptoms

Headache
Confusion and personality changes
Partial visual field losses
Unilateral or bilateral hearing loss
Balance problems and dizziness
Neuropsychiatric findings
Cognitive function disorders

Risk Factors

Female sex (20-40 years)
Autoimmune disease background
Family history (rarely)

When to See a Doctor?

If you experience any of the following symptoms, seek medical attention promptly:

  • Sudden visual field defect
  • Unexplained hearing loss
  • Headache with behavioral and memory disorders
  • Transient confusion episodes
  • Typical lesions on MRI in corpus callosum

Treatment Methods

01
High-dose intravenous methylprednisolone
02
IVIG therapy
03
Cyclophosphamide in resistant cases
04
Mycophenolate mofetil
05
Rituximab
06
Hearing aid and rehabilitation

Which Department to Visit?

You can visit our Nöroloji department for these complaints. Our specialist physicians will create the most suitable treatment plan for you.

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Let us help you

You can make an appointment with our specialists or contact us for your concerns.

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Health Disclaimer: The information on this page is prepared for general informational purposes only. It does not replace medical diagnosis and treatment. Please consult your physician for your complaints. Saygı Hospital does not accept responsibility for actions taken based on the information on this page.