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Port Wine Stain (Nevus Flammeus)

A persistent flat red-purple capillary malformation present from birth.

Written by: Saygı Hospital Health Guide Editorial Board
Last updated:

This content has been compiled by the Saygı Hospital Health Guide Editorial Board and is periodically reviewed by a specialist physician.

References (5)

This content is for informational purposes only and does not constitute medical advice. You can book an appointment at our Dermatoloji department. Book Appointment →

What is Port Wine Stain (Nevus Flammeus)?

Port wine stain (nevus flammeus) is a congenital capillary malformation due to permanent dilatation of dermal vessels. It is most commonly associated with the GNAQ gene mutation.

It is not raised above the surface; over time it may darken with age, thicken and develop nodular areas. Some lesions on the face (trigeminal V1 distribution) may be the cutaneous finding of Sturge-Weber syndrome.

Pulsed-dye laser is the standard approach in treatment, and starting at an early age provides better results.

Symptoms

Congenital flat red-purple patch
Location on the face, neck and extremities
Darkening with growth
Thickening and nodular areas
Skin atrophy and overgrowth (some cases)
Sturge-Weber: epilepsy, glaucoma, neurological problems
Klippel-Trenaunay association (extremity)

Risk Factors

Somatic GNAQ mutation
Early embryonic vascular development disturbance
Family history (rare)
Sturge-Weber risk with facial location
Syndromic capillary malformations
Birth events and pregnancy factors
Coexistence with other vascular malformations

When to See a Doctor?

If you experience any of the following symptoms, seek medical attention promptly:

  • When red-purple patches are noticed at birth
  • If lesions cover one-half of the face
  • On suspicion of seizure or increased intraocular pressure
  • When bleeding and thickening develop in the lesion
  • When applying to pediatric dermatology for treatment planning

Treatment Methods

01
Pulsed-dye laser (gold standard)
02
Initiation of treatment at an early age
03
Neurology and ophthalmology evaluation (suspected Sturge-Weber)
04
Brain MRI (selected cases)
05
Psychosocial support
06
Camouflage makeup and care recommendations

Which Department to Visit?

You can visit our Dermatoloji department for these complaints. Our specialist physicians will create the most suitable treatment plan for you.

Learn About Dermatoloji Department

Let us help you

You can make an appointment with our specialists or contact us for your concerns.

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Health Disclaimer: The information on this page is prepared for general informational purposes only. It does not replace medical diagnosis and treatment. Please consult your physician for your complaints. Saygı Hospital does not accept responsibility for actions taken based on the information on this page.